Hereditary gingival fibromatosis is a rare condition, affecting only one in 750,000 people (Fletcher, 1966). It usually develops as an isolated disorder but can be one feature of a syndrome. In their review of various syndromes, Gorlin and colleagues (1990) identified hypertrichosis as the characteristic most often seen with syndromic HGF (Hereditary Gingival Fibromatosis) and noted that HGF is occasionally associated with mental retardation and epilepsy. HGF is usually identified as an autosomal dominant condition, though recessive forms are described in the literature. The hyperplastic gingiva is usually of normal color and has a firm consistency, with abundant stippling on the adjacent gingiva.