Congenital lower lip pits have been reported in about 0.001% of the population. They are usually bilateral but may be unilateral or centrally placed on the vermilion border of the lower lip. Lip pits are a rare congenital invagination of the lower lip. A higher incidence has been reported in females, but no genetic sex linkage has been found. It has been suggested that the genetic defect of lip pits is due to a microdeletion on chromosome bands 1q32-q41 [1, 2, 3, 4, 10].